Question 1

A patient with hemophilia A is undergoing a tooth extraction at the dentist's office. As an adjunct to factor VIII, what other drug should the nurse anticipate being ordered for this patient?

Accepted Answer

A)   Tranexamic acid [Cyklokapron]
B)   Acetaminophen [Tylenol]
C)   Desmopressin [Stimate]
D)   Vitamin KE) C) and D)
F) A) and C)

Question 2

A patient with hemophilia B is admitted to the hospital for surgery. The patient's history reveals long-term use of factor replacement as prophylaxis for bleeding episodes. The nurse anticipates that the provider will order which medication to prevent excessive perioperative bleeding?

Accepted Answer

A)   Desmopressin
B)   Factor VIII
C)   Ibuprofen
D)   Tranexamic acidE) B) and C)
F) A) and D)

Question 3

A patient with epistaxis and a history of hemophilia A is admitted to the unit and is scheduled for replacement therapy. The nurse should prepare to administer which medication?

Accepted Answer

A)   Tranexamic acid [Cyklokapron]
B)   Aminocaproic acid [Amicar]
C)   Desmopressin [Stimate]
D)   Factor VIIIE) B) and C)
F) A) and D) D

Question 4

A patient who is receiving a factor VIII concentrate to treat hemophilia A develops hives, a low-grade temperature elevation, and a stuffy nose. The nurse will prepare to:

Accepted Answer

A)   administer subcutaneous epinephrine.
B)   give an antipyretic medication.
C)   give oral diphenhydramine.
D)   provide respiratory support.E) B) and C)
F) A) and D)

Question 5

The nurse is conducting a nursing education class on hemophilia. The nurse correctly states that which characteristics are most likely to be seen in a patient with hemophilia?

Accepted Answer

A)   Male gender
B)   Female gender
C)   Mother is a carrier.
D)   All races and ethnicities are susceptible.
E)   Both parents are carriers.F) A) and D)
G) A) and B)

Question 6

A nurse is caring for a child who has hemophilia. While reviewing this child's immunization records, the nurse notes that the child needs the tetanus and reduced diphtheria toxoids and acellular pertussis (Tdap)  vaccine and the hepatitis A vaccine. The nurse should notify the provider and obtain an order to give:

Accepted Answer

A)   both vaccines intramuscularly.
B)   both vaccines subcutaneously.
C)   the hepatitis A vaccine only subcutaneously.
D)   the Tdap vaccine only intramuscularly.E) A) and D)
F) A) and C)

Question 7

A child with severe hemophilia A receives factor VIII. The nurse expects this drug to be given:

Accepted Answer

A)   on demand when bleeding occurs.
B)   on demand when plasma factor VIII activity is less than 1% above normal.
C)   prophylactically once weekly to maintain normal factor VIII activity.
D)   prophylactically 3 times weekly to maintain factor VIII activity above 1% of normal.E) A) and C)
F) B) and D)

Question 8

The parents of a boy with hemophilia A want to know why their son will receive factor replacement on an ongoing basis rather than when needed for bleeding episodes. They tell the nurse that the boy's grandfather, who had the same disease, received the drug only when he had bleeding. The nurse will give the parents which information about ongoing therapy?

Accepted Answer

A)   It can reverse progression of the disease.
B)   It is cheaper, because the amounts of the drug used are less.
C)   It is used to minimize long-term damage to the joints.
D)   It prevents the development of inhibitors.E) A) and B)
F) A) and C)

Question 9

A child with moderate hemophilia A who weighs 20 kg is admitted to the hospital after a knee injury with bleeding into the joint. The nurse will expect the provider to order which medication?

Accepted Answer

A)   Advate 400 units IV over 10 minutes
B)   Benefix 800 units slow IV push
C)   Desmopressin 6 mcg IV over 15 to 30 minutes
D)   Tranexamic acid [Cyklokapron] 200 mg IVE) A) and B)
F) B) and C)

Question 10

A nurse is caring for an African American patient with severe hemophilia A who has been admitted for bleeding into the knee joint. The prescriber has ordered intravenous factor VIIa [NovoSeven RT]. A nursing student wants to know why this patient is not receiving factor VIII. Which statement by the nurse is correct?

Accepted Answer

A)   "Factor VIIa is stronger than factor VIII and will work faster."
B)   "Factor VIII is used for prophylaxis, and factor VIIa is used for acute episodes."
C)   "Factor VIIa is used when patients develop antibodies against factor VIII."
D)   "Factor VIIa provides immune tolerance therapy so that factor VIII will be more effective."E) None of the above
F) B) and C)

Question 11

A child with hemophilia A who weighs 30 kg receives factor VIII on an ongoing basis as prophylaxis. The provider orders desmopressin [Stimate] to be used for nosebleeds. The nurse will instruct the child's parents to give the medication as ____ nostril as needed.

Accepted Answer

A)   1 spray in each
B)   1 spray in one
C)   2 sprays in each
D)   2 sprays in oneE) A) and B)
F) None of the above B

Question 12

A patient with hemophilia is hospitalized for infusion of factor VIII replacement through a venous port. While giving the drug, the nurse notes that the patient's temperature is 101.5°F. The nurse will contact the provider to report which possibility?

Accepted Answer

A)   Anaphylactic reaction
B)   Contamination of factor replacement
C)   Port infection
D)   Thrombolytic eventE) B) and C)
F) A) and B) C

Exam 54: Drugs for Hemophilia

A patient with hemophilia A is undergoing a tooth extraction at the dentist's office. As an adjunct to factor VIII, what other drug should the nurse anticipate being ordered for this patient?

Correct Answer
verified

A patient with hemophilia B is admitted to the hospital for surgery. The patient's history reveals long-term use of factor replacement as prophylaxis for bleeding episodes. The nurse anticipates that the provider will order which medication to prevent excessive perioperative bleeding?

Correct Answer
verified

A patient with epistaxis and a history of hemophilia A is admitted to the unit and is scheduled for replacement therapy. The nurse should prepare to administer which medication?

Correct Answer
verified
D

A patient who is receiving a factor VIII concentrate to treat hemophilia A develops hives, a low-grade temperature elevation, and a stuffy nose. The nurse will prepare to:

Correct Answer
verified

The nurse is conducting a nursing education class on hemophilia. The nurse correctly states that which characteristics are most likely to be seen in a patient with hemophilia?

Correct Answer
verified

Correct Answer
verified

A child with severe hemophilia A receives factor VIII. The nurse expects this drug to be given:

Correct Answer
verified

Correct Answer
verified

A child with moderate hemophilia A who weighs 20 kg is admitted to the hospital after a knee injury with bleeding into the joint. The nurse will expect the provider to order which medication?

Correct Answer
verified

Correct Answer
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A child with hemophilia A who weighs 30 kg receives factor VIII on an ongoing basis as prophylaxis. The provider orders desmopressin [Stimate] to be used for nosebleeds. The nurse will instruct the child's parents to give the medication as ____ nostril as needed.

Correct Answer
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B

A patient with hemophilia is hospitalized for infusion of factor VIII replacement through a venous port. While giving the drug, the nurse notes that the patient's temperature is 101.5°F. The nurse will contact the provider to report which possibility?

Correct Answer
verified
C

Exam 54: Drugs for Hemophilia

A patient with hemophilia A is undergoing a tooth extraction at the dentist's office. As an adjunct to factor VIII, what other drug should the nurse anticipate being ordered for this patient?

Correct AnswerverifiedShow Answer

A patient with hemophilia B is admitted to the hospital for surgery. The patient's history reveals long-term use of factor replacement as prophylaxis for bleeding episodes. The nurse anticipates that the provider will order which medication to prevent excessive perioperative bleeding?

Correct AnswerverifiedShow Answer

A patient with epistaxis and a history of hemophilia A is admitted to the unit and is scheduled for replacement therapy. The nurse should prepare to administer which medication?

Correct AnswerverifiedD

A patient who is receiving a factor VIII concentrate to treat hemophilia A develops hives, a low-grade temperature elevation, and a stuffy nose. The nurse will prepare to:

Correct AnswerverifiedShow Answer

The nurse is conducting a nursing education class on hemophilia. The nurse correctly states that which characteristics are most likely to be seen in a patient with hemophilia?

Correct AnswerverifiedShow Answer

Correct AnswerverifiedShow Answer

A child with severe hemophilia A receives factor VIII. The nurse expects this drug to be given:

Correct AnswerverifiedShow Answer

Correct AnswerverifiedShow Answer

A child with moderate hemophilia A who weighs 20 kg is admitted to the hospital after a knee injury with bleeding into the joint. The nurse will expect the provider to order which medication?

Correct AnswerverifiedShow Answer

Correct AnswerverifiedShow Answer

A child with hemophilia A who weighs 30 kg receives factor VIII on an ongoing basis as prophylaxis. The provider orders desmopressin [Stimate] to be used for nosebleeds. The nurse will instruct the child's parents to give the medication as ____ nostril as needed.

Correct AnswerverifiedB

A patient with hemophilia is hospitalized for infusion of factor VIII replacement through a venous port. While giving the drug, the nurse notes that the patient's temperature is 101.5°F. The nurse will contact the provider to report which possibility?

Correct AnswerverifiedC

Correct Answer
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D

Correct Answer
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B

Correct Answer
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C